CAAP1

Chr 9

caspase activity and apoptosis inhibitor 1

The CAAP1 protein functions as an anti-apoptotic protein that modulates a caspase-10 dependent mitochondrial caspase-3/9 feedback amplification loop. Mutations in this highly constrained gene cause autosomal recessive neurodegeneration with brain atrophy. The inheritance pattern is autosomal recessive.

ResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.46
Clinical SummaryCAAP1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.78) — some intolerance to loss-of-function variants.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.46LOEUF
pLI 0.784
Z-score 2.95
OE 0.14 (0.060.46)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
-0.47Z-score
OE missense 1.10 (0.981.23)
207 obs / 188.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.14 (0.060.46)
00.351.4
Missense OE1.10 (0.981.23)
00.61.4
Synonymous OE1.30
01.21.6
LoF obs/exp: 2 / 13.8Missense obs/exp: 207 / 188.7Syn Z: -1.99
DN
0.3991th %ile
GOF
0.3887th %ile
LOF
0.69top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.46

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CAAP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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