CA8

Chr 8AR

carbonic anhydrase 8 (inactive)

Also known as: CA-RP, CA-VIII, CALS, CAMRQ3, CARP, SCAR34

CA8 encodes a catalytically inactive carbonic anhydrase that localizes to the cerebellum and appears important for cerebellar function. Mutations cause autosomal recessive spinocerebellar ataxia type 34, which involves cerebellar dysfunction and movement disorders. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.67), suggesting some intolerance to complete loss of function.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.671 OMIM phenotype
Clinical SummaryCA8
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Gene-Disease Validity (ClinGen)
cerebellar ataxia · ARModerate

Moderate evidence — consider for supplementary testing

Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.67LOEUF
pLI 0.008
Z-score 2.64
OE 0.36 (0.200.67)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.24Z-score
OE missense 0.72 (0.620.84)
115 obs / 159.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.36 (0.200.67)
00.351.4
Missense OE0.72 (0.620.84)
00.61.4
Synonymous OE1.01
01.21.6
LoF obs/exp: 7 / 19.6Missense obs/exp: 115 / 159.0Syn Z: -0.07
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitiveCA8-related cerebellar ataxia, intellectual developmental disorder, and dysequilibrium syndromeLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.74top 25%
GOF
0.5954th %ile
LOF
0.2190th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CA8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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