C1ORF87

Chr 1

chromosome 1 open reading frame 87

Also known as: CREF

The protein encoded by this gene has an unknown function. Mutations cause autosomal recessive spastic paraplegia with intellectual disability, characterized by progressive spasticity of the lower limbs and cognitive impairment typically manifesting in early childhood. The gene shows very low constraint against loss-of-function variants, suggesting tolerance to such mutations in the general population.

LOEUF 1.68
Clinical SummaryC1ORF87
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.68LOEUF
pLI 0.000
Z-score -1.24
OE 1.26 (0.951.68)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.21Z-score
OE missense 1.04 (0.941.14)
293 obs / 282.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.26 (0.951.68)
00.351.4
Missense OE1.04 (0.941.14)
00.61.4
Synonymous OE1.09
01.21.6
LoF obs/exp: 33 / 26.2Missense obs/exp: 293 / 282.8Syn Z: -0.75

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

C1ORF87 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found