C1ORF210

Chr 1

chromosome 1 open reading frame 210

Also known as: TEMP

This protein is predicted to be involved in membrane trafficking between endosomes and the plasma membrane. Mutations in C1ORF210 cause autosomal recessive developmental and epileptic encephalopathy with microcephaly. The gene is highly intolerant to loss-of-function variants, suggesting that complete loss of protein function is likely pathogenic.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.91
Clinical SummaryC1ORF210
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
11 unique Pathogenic / Likely Pathogenic· 3 VUS of 18 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.91LOEUF
pLI 0.000
Z-score -0.55
OE 1.30 (0.641.91)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.06Z-score
OE missense 0.98 (0.811.20)
70 obs / 71.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.30 (0.641.91)
00.351.4
Missense OE0.98 (0.811.20)
00.61.4
Synonymous OE1.01
01.21.6
LoF obs/exp: 5 / 3.8Missense obs/exp: 70 / 71.3Syn Z: -0.04

ClinVar Variant Classifications

18 submitted variants in ClinVar

Classification Summary

Pathogenic10
Likely Pathogenic1
VUS3
Likely Benign1
10
Pathogenic
1
Likely Pathogenic
3
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
10
Likely Pathogenic
1
VUS
3
Likely Benign
1
Benign
0
Total15

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

C1ORF210 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found