C1ORF122

Chr 1

chromosome 1 open reading frame 122

Also known as: ALAESM

The protein encoded by this gene has unknown function but is thought to be involved in cellular processes. Mutations cause autosomal recessive spastic paraplegia, characterized by progressive lower limb spasticity and weakness typically beginning in childhood or adolescence. This gene shows relatively low constraint against loss-of-function variants, which is consistent with its recessive inheritance pattern.

LOEUF 1.76
Clinical SummaryC1ORF122
Population Constraint (gnomAD)
Low constraint (pLI 0.14) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.76LOEUF
pLI 0.143
Z-score 0.63
OE 0.51 (0.171.76)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.43Z-score
OE missense 0.79 (0.581.09)
27 obs / 34.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.51 (0.171.76)
00.351.4
Missense OE0.79 (0.581.09)
00.61.4
Synonymous OE0.54
01.21.6
LoF obs/exp: 1 / 1.9Missense obs/exp: 27 / 34.0Syn Z: 1.46

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

C1ORF122 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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