C18ORF54

Chr 18

chromosome 18 open reading frame 54

Also known as: LAS2

The protein is predicted to negatively regulate cell population proliferation and is located in the extracellular region. Mutations in this gene cause developmental delays and intellectual disability with autosomal recessive inheritance. This gene is highly constrained against loss-of-function variants, suggesting that complete loss of protein function is likely pathogenic.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
2
Pubs (1 yr)
55
P/LP submissions
P/LP missense
1.16
LOEUF
Mechanism
Clinical SummaryC18ORF54
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
53 unique Pathogenic / Likely Pathogenic· 3 VUS of 68 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.16LOEUF
pLI 0.000
Z-score 1.11
OE 0.70 (0.441.16)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.57Z-score
OE missense 1.11 (1.001.25)
218 obs / 195.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.70 (0.441.16)
00.351.4
Missense OE1.11 (1.001.25)
00.61.4
Synonymous OE0.95
01.21.6
LoF obs/exp: 11 / 15.8Missense obs/exp: 218 / 195.7Syn Z: 0.35

ClinVar Variant Classifications

68 submitted variants in ClinVar

Classification Summary

Pathogenic51
Likely Pathogenic2
VUS3
Likely Benign2
51
Pathogenic
2
Likely Pathogenic
3
VUS
2
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
51
Likely Pathogenic
2
VUS
3
Likely Benign
2
Benign
0
Total58

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

C18ORF54 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →