C17ORF100

Chr 17

chromosome 17 open reading frame 100

I notice that no information has been provided about the C17ORF100 gene - there are no details about the protein function, associated diseases, inheritance patterns, or constraint metrics. Without this essential information, I cannot write an accurate clinical gene summary following the strict rules you've outlined. Please provide the relevant gene data including protein function, phenotype associations, inheritance pattern, and any available constraint scores so I can create an appropriate 2-3 sentence summary for the pediatric neurogenetics portal.

LOEUF 1.79
Clinical SummaryC17ORF100
Population Constraint (gnomAD)
Low constraint (pLI 0.13) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
20 unique Pathogenic / Likely Pathogenic· 6 VUS of 26 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.79LOEUF
pLI 0.131
Z-score 0.52
OE 0.57 (0.191.79)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.55Z-score
OE missense 0.85 (0.711.01)
86 obs / 101.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.57 (0.191.79)
00.351.4
Missense OE0.85 (0.711.01)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 1 / 1.7Missense obs/exp: 86 / 101.7Syn Z: 0.43

ClinVar Variant Classifications

26 submitted variants in ClinVar

Classification Summary

Pathogenic19
Likely Pathogenic1
VUS6
19
Pathogenic
1
Likely Pathogenic
6
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
19
Likely Pathogenic
1
VUS
6
Likely Benign
0
Benign
0
Total26

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

C17ORF100 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found