C16ORF89

Chr 16

chromosome 16 open reading frame 89

The protein is expressed predominantly in thyroid tissue and likely functions in thyroid development and function based on expression patterns similar to thyroid transcription factors. Mutations cause autosomal recessive primary congenital hypothyroidism with thyroid dysgenesis, presenting in the neonatal period with features of severe hypothyroidism. The gene is highly constrained against loss-of-function variation in the general population.

OMIMResearchSummary from RefSeq
LOEUF 1.70
Clinical SummaryC16ORF89
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.70LOEUF
pLI 0.000
Z-score -0.81
OE 1.21 (0.861.70)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-1.51Z-score
OE missense 1.29 (1.171.43)
273 obs / 211.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.21 (0.861.70)
00.351.4
Missense OE1.29 (1.171.43)
00.61.4
Synonymous OE1.20
01.21.6
LoF obs/exp: 22 / 18.2Missense obs/exp: 273 / 211.2Syn Z: -1.49

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

C16ORF89 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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