C12ORF56

Chr 12

chromosome 12 open reading frame 56

The protein encoded by this gene is poorly characterized, with limited functional data available. Biallelic mutations cause a severe neurodevelopmental disorder characterized by global developmental delay, intellectual disability, seizures, and brain malformations including microcephaly and corpus callosum abnormalities. This follows an autosomal recessive inheritance pattern with early childhood onset of neurological symptoms.

LOEUF 1.58
Clinical SummaryC12ORF56
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.58LOEUF
pLI 0.000
Z-score -0.45
OE 1.11 (0.791.58)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.12Z-score
OE missense 0.98 (0.881.09)
227 obs / 232.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.11 (0.791.58)
00.351.4
Missense OE0.98 (0.881.09)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 22 / 19.8Missense obs/exp: 227 / 232.3Syn Z: 0.51

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

C12ORF56 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found