C10ORF71

Chr 10AD

chromosome 10 open reading frame 71

Also known as: CEFIP, CMD1QQ

This protein activates the calcineurin/NFAT signaling pathway in cardiomyocytes and regulates myocardium morphogenesis, mass, and contractile function. Mutations cause autosomal dominant dilated cardiomyopathy (type 1QQ), primarily affecting cardiac muscle function and structure.

Summary from RefSeq, OMIM, UniProt
Research Assistant →

Primary Disease Associations & Inheritance

Cardiomyopathy, dilated, 1QQMIM #621251
AD
0
Active trials
2
Pubs (1 yr)
64
P/LP submissions
0%
P/LP missense
0.80
LOEUF
Mechanism
Clinical SummaryC10ORF71
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
64 unique Pathogenic / Likely Pathogenic· 45 VUS of 121 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.80LOEUF
pLI 0.000
Z-score 2.49
OE 0.55 (0.390.80)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.69Z-score
OE missense 0.93 (0.880.99)
765 obs / 820.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.55 (0.390.80)
00.351.4
Missense OE0.93 (0.880.99)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 20 / 36.2Missense obs/exp: 765 / 820.3Syn Z: 1.10

ClinVar Variant Classifications

121 submitted variants in ClinVar

Classification Summary

Pathogenic42
Likely Pathogenic22
VUS45
Likely Benign1
Benign7
42
Pathogenic
22
Likely Pathogenic
45
VUS
1
Likely Benign
7
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
3
0
39
0
42
Likely Pathogenic
0
0
22
0
22
VUS
1
14
30
0
45
Likely Benign
0
1
0
0
1
Benign
0
5
0
2
7
Total420912117

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

C10ORF71 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC