Ensembl is currently experiencing issues

The Ensembl REST API is temporarily unavailable. Some gene data (transcript details, protein domains) may be incomplete. Other data sources are unaffected.

You can check Ensembl's status at status.ensembl.org

BRRIAR

Chr 3

BHLHE40 and RIG-I regulating ITPR1 antisense RNA

I apologize, but I cannot write a clinical gene summary for BRRIAR because no information about this gene was provided in your message. To create an accurate summary following your strict requirements, I would need specific data about the protein function, associated diseases, inheritance patterns, and any relevant clinical features or constraint metrics for this gene.

Clinical SummaryBRRIAR
📋
ClinVar Variants
41 unique Pathogenic / Likely Pathogenic· 35 VUS of 111 total submissions
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/BRRIAR?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

111 submitted variants in ClinVar

Classification Summary

Pathogenic38
Likely Pathogenic3
VUS35
Likely Benign27
Benign4
Conflicting3
38
Pathogenic
3
Likely Pathogenic
35
VUS
27
Likely Benign
4
Benign
3
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
1
0
37
0
38
Likely Pathogenic
1
1
1
0
3
VUS
0
30
4
1
35
Likely Benign
0
0
14
13
27
Benign
0
0
4
0
4
Conflicting
3
Total2316014110

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

BRRIAR · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found