BOP1

Chr 8

BOP1 ribosomal biogenesis factor

Enables RNA binding activity. Involved in regulation of cell cycle; regulation of signal transduction by p53 class mediator; and ribosomal large subunit biogenesis. Located in chromosome; nucleolus; and nucleoplasm. Part of PeBoW complex. [provided by Alliance of Genome Resources, Jul 2025]

0
Active trials
9
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.32
LOEUF
DN
Mechanism· predicted
Clinical SummaryBOP1
Population Constraint (gnomAD)
Low constraint (pLI 0.09) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.32LOEUF
pLI 0.093
Z-score 1.15
OE 0.43 (0.171.32)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.26Z-score
OE missense 1.09 (0.911.32)
77 obs / 70.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.43 (0.171.32)
00.351.4
Missense OE1.09 (0.911.32)
00.61.4
Synonymous OE1.24
01.21.6
LoF obs/exp: 2 / 4.7Missense obs/exp: 77 / 70.7Syn Z: -1.09
DN
0.6647th %ile
GOF
0.5857th %ile
LOF
0.4038th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

BOP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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