BOLA2

Chr 16

bolA family member 2

Also known as: BOLA2A, My016

BOLA2 encodes a cytosolic iron-sulfur cluster assembly factor that facilitates [2Fe-2S] cluster insertion into cytosolic proteins, working together with the monothiol glutaredoxin GLRX3. Mutations cause multiple mitochondrial dysfunctions syndrome 2, an autosomal recessive disorder characterized by early-onset mitochondrial dysfunction affecting multiple organ systems. The gene is located within a segmental duplication region on chromosome 16 and has high sequence similarity to BOLA2B.

OMIMResearchSummary from RefSeq, UniProt
Clinical SummaryBOLA2
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ClinVar Variants
77 unique Pathogenic / Likely Pathogenic· 9 VUS of 89 total submissions

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

89 submitted variants in ClinVar

Classification Summary

Pathogenic70
Likely Pathogenic7
VUS9
Benign2
70
Pathogenic
7
Likely Pathogenic
9
VUS
2
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
70
Likely Pathogenic
7
VUS
9
Likely Benign
0
Benign
2
Total88

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

BOLA2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗