BIN1

Chr 2AR

bridging integrator 1

Also known as: AMPH2, AMPHL, CNM2, SH3P9

The protein functions as a nucleocytoplasmic adaptor involved in synaptic vesicle endocytosis in the central nervous system and localizes to muscle cytoplasm and nucleus where it can activate apoptotic processes. Mutations cause centronuclear myopathy 2, inherited in an autosomal recessive pattern. The high constraint scores (pLI 0.78, LOEUF 0.37) indicate the gene is intolerant to loss-of-function variants, consistent with pathogenicity through loss of normal protein function.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.371 OMIM phenotype
Clinical SummaryBIN1
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Gene-Disease Validity (ClinGen)
centronuclear myopathy · ADLimited

Limited evidence — not for standalone diagnostic reporting

2 total gene-disease associations curated

Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.78) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.37LOEUF
pLI 0.778
Z-score 4.46
OE 0.20 (0.110.37)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.25Z-score
OE missense 0.66 (0.600.74)
235 obs / 354.2 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.20 (0.110.37)
00.351.4
Missense OE0.66 (0.600.74)
00.61.4
Synonymous OE0.97
01.21.6
LoF obs/exp: 7 / 35.8Missense obs/exp: 235 / 354.2Syn Z: 0.26

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

BIN1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗