BCLAF3

Chr X

BCLAF1 and THRAP3 family member 3

Also known as: CXorf23, TOBF1

BCLAF3 encodes a component of the spliceosome complex that is important for maintaining embryonic stem cell fate and may regulate Wnt-driven epithelial renewal in gastric mucosa. The gene is highly constrained against loss-of-function variants (LOEUF 0.421), suggesting mutations would likely cause severe developmental phenotypes. No specific disease associations have been established for this gene based on the provided information.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.42
LOEUF
LOF
Mechanism· predicted
Clinical SummaryBCLAF3
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.63) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.42LOEUF
pLI 0.625
Z-score 3.70
OE 0.20 (0.100.42)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.26Z-score
OE missense 0.77 (0.690.87)
190 obs / 245.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.20 (0.100.42)
00.351.4
Missense OE0.77 (0.690.87)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 5 / 25.0Missense obs/exp: 190 / 245.7Syn Z: 0.50
DN
0.2997th %ile
GOF
0.2298th %ile
LOF
0.77top 5%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.42

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

BCLAF3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found