BCL7C

Chr 16

BAF chromatin remodeling complex subunit BCL7C

Also known as: SMARCJ3

The BCL7C protein may have anti-apoptotic functions, though its precise cellular role remains unclear. Mutations in BCL7C cause neurodevelopmental disorders with intellectual disability and developmental delay. BCL7C follows autosomal recessive inheritance and is not highly constrained against loss-of-function variants.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.72
Clinical SummaryBCL7C
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.32) despite low pLI — interpret in context.
📋
ClinVar Variants
11 unique Pathogenic / Likely Pathogenic· 38 VUS of 58 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.72LOEUF
pLI 0.080
Z-score 2.26
OE 0.32 (0.150.72)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.98Z-score
OE missense 0.77 (0.660.90)
111 obs / 144.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.32 (0.150.72)
00.351.4
Missense OE0.77 (0.660.90)
00.61.4
Synonymous OE0.87
01.21.6
LoF obs/exp: 4 / 12.7Missense obs/exp: 111 / 144.0Syn Z: 0.78

ClinVar Variant Classifications

58 submitted variants in ClinVar

Classification Summary

Pathogenic10
Likely Pathogenic1
VUS38
Likely Benign1
10
Pathogenic
1
Likely Pathogenic
38
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
10
0
10
Likely Pathogenic
0
0
1
0
1
VUS
0
29
9
0
38
Likely Benign
0
1
0
0
1
Benign
0
0
0
0
0
Total03020050

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

BCL7C · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 4 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC