BCL7B

Chr 7

BAF chromatin remodeling complex subunit BCL7B

The protein encoded by this gene positively regulates apoptosis, negatively regulates Wnt signaling components CTNNB1 and HMGA1, and is involved in cell cycle progression and stem cell differentiation. BCL7B is located in a chromosomal region commonly deleted in Williams syndrome, though specific disease associations with isolated BCL7B mutations are not well-established in the provided data. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.714).

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 0.71
Clinical SummaryBCL7B
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.28) despite low pLI — interpret in context.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.71LOEUF
pLI 0.185
Z-score 2.21
OE 0.28 (0.130.71)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.22Z-score
OE missense 0.68 (0.560.82)
77 obs / 113.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.28 (0.130.71)
00.351.4
Missense OE0.68 (0.560.82)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 3 / 10.9Missense obs/exp: 77 / 113.5Syn Z: 0.01
DN
0.6648th %ile
GOF
0.5071th %ile
LOF
0.4430th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

BCL7B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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