BCCIP

Chr 10

BRCA2 and CDKN1A interacting protein

Also known as: TOK-1, TOK1

BCCIP encodes a nuclear protein that functions as a cofactor for BRCA2 in DNA homologous recombination repair and regulates microtubule organization and spindle pole stability during cell division. Mutations cause an autosomal recessive neurodevelopmental disorder with microcephaly, intellectual disability, and growth retardation. The gene shows low constraint against loss-of-function variants, consistent with recessive inheritance where heterozygous carriers are typically unaffected.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.78
Clinical SummaryBCCIP
Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.78LOEUF
pLI 0.008
Z-score 2.17
OE 0.40 (0.220.78)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.10Z-score
OE missense 1.02 (0.901.16)
175 obs / 171.4 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.40 (0.220.78)
00.351.4
Missense OE1.02 (0.901.16)
00.61.4
Synonymous OE0.94
01.21.6
LoF obs/exp: 6 / 15.1Missense obs/exp: 175 / 171.4Syn Z: 0.42

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

BCCIP · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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