BCAS3

Chr 17AR

BCAS3 microtubule associated cell migration factor

Also known as: GAOB1, HEMARS, MAAB, PHAF2

BCAS3 encodes a protein that regulates cell polarity and directional migration through CDC42 activation and actin cytoskeleton reorganization, functions as a transcriptional coactivator for estrogen-responsive genes, and plays a regulatory role in autophagy. Mutations cause Hengel-Maroofian-Schols syndrome with autosomal recessive inheritance. The gene is highly constrained against loss-of-function variants (LOEUF 0.467), indicating that complete loss of protein function is likely detrimental.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismARLOEUF 0.471 OMIM phenotype
Clinical SummaryBCAS3
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.31) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.47LOEUF
pLI 0.000
Z-score 4.80
OE 0.31 (0.220.47)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.60Z-score
OE missense 0.69 (0.630.75)
375 obs / 546.0 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.31 (0.220.47)
00.351.4
Missense OE0.69 (0.630.75)
00.61.4
Synonymous OE0.98
01.21.6
LoF obs/exp: 18 / 57.2Missense obs/exp: 375 / 546.0Syn Z: 0.23

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

BCAS3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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