ATXN8OS

Chr 13ADMulti

ATXN8 opposite strand lncRNA

Also known as: KLHL1AS, NCRNA00003, SCA8

This gene is an antisense transcript to the KLHL1 gene (homolog to the Drosophila KELCH gene); it does not itself appear to be protein coding. A TAC/TGC trinucleotide repeat expansion that is incorporated into this gene transcript, but not the KLHL1 transcript, causes spinocerebellar ataxia type 8. Presumably the expansion interferes with normal antisense function of this transcript. [provided by RefSeq, Oct 2008]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

{Parkinson disease, susceptibility to}MIM #168600
ADMulti
Spinocerebellar ataxia 8MIM #608768
AD
2
Active trials
19
Pubs (1 yr)
P/LP submissions
P/LP missense
LOEUF
Multiple*
Mechanism· predicted
📖
GeneReview available — ATXN8OS
Authoritative clinical overview · Recommended first read
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Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ATXN8OS · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.