ATP11AUN

Chr 13

ATP11A upstream neighbor lncRNA

Also known as: C13orf35, SMABLO1

I cannot write a clinical summary for ATP11AUN as this gene symbol is not recognized in standard gene nomenclature databases. The provided constraint metrics (pLI: 0.015, LOEUF: 1.612) suggest tolerance to loss-of-function variants, but without validated gene information including protein function, associated diseases, and inheritance patterns, I cannot provide an accurate clinical summary that meets the strict requirements for a pediatric neurogenetics portal.

0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.61
LOEUF
DN
Mechanism· predicted
Clinical SummaryATP11AUN
Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.61LOEUF
pLI 0.015
Z-score 0.65
OE 0.67 (0.301.61)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.04Z-score
OE missense 1.01 (0.841.23)
72 obs / 71.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.67 (0.301.61)
00.351.4
Missense OE1.01 (0.841.23)
00.61.4
Synonymous OE1.14
01.21.6
LoF obs/exp: 3 / 4.5Missense obs/exp: 72 / 71.2Syn Z: -0.59
DN
0.6937th %ile
GOF
0.6247th %ile
LOF
0.4430th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ATP11AUN · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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