ATF7IP2

Chr 16

activating transcription factor 7 interacting protein 2

Also known as: MCAF2

The protein functions as a transcriptional recruiter that couples transcription factors to general transcription machinery and modulates chromatin formation, acting as either an activator or repressor depending on context. Mutations in this gene cause autosomal recessive intellectual disability with seizures and microcephaly, typically presenting in early childhood. The gene shows moderate constraint against loss-of-function variants, suggesting some intolerance to complete protein loss.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.47
Clinical SummaryATF7IP2
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.25) despite low pLI — interpret in context.
📋
ClinVar Variants
19 unique Pathogenic / Likely Pathogenic· 128 VUS of 183 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.47LOEUF
pLI 0.158
Z-score 3.67
OE 0.25 (0.140.47)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
-1.32Z-score
OE missense 1.20 (1.111.30)
409 obs / 340.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.25 (0.140.47)
00.351.4
Missense OE1.20 (1.111.30)
00.61.4
Synonymous OE1.18
01.21.6
LoF obs/exp: 7 / 27.9Missense obs/exp: 409 / 340.5Syn Z: -1.52

ClinVar Variant Classifications

183 submitted variants in ClinVar

Classification Summary

Pathogenic19
VUS128
Likely Benign18
Conflicting1
19
Pathogenic
128
VUS
18
Likely Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
19
0
19
Likely Pathogenic
0
0
0
0
0
VUS
2
98
28
0
128
Likely Benign
0
13
4
1
18
Benign
0
0
0
0
0
Conflicting
1
Total2111511166

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ATF7IP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC