ATCAY

Chr 19AR

ATCAY kinesin light chain interacting caytaxin

This gene encodes a neuron-restricted protein containing a CRAL-TRIO motif that functions in cerebellar cortex development and may regulate glutaminase enzyme activity for glutamate neurotransmitter production or mitochondrial localization within neurons. Mutations cause cerebellar ataxia, Cayman type, inherited in an autosomal recessive pattern. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.446), reflecting its importance in neuronal function.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.452 OMIM phenotypes
Clinical SummaryATCAY
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.62) — some intolerance to loss-of-function variants.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.45LOEUF
pLI 0.621
Z-score 3.38
OE 0.20 (0.100.45)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.61Z-score
OE missense 0.72 (0.640.81)
185 obs / 257.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.20 (0.100.45)
00.351.4
Missense OE0.72 (0.640.81)
00.61.4
Synonymous OE1.05
01.21.6
LoF obs/exp: 4 / 20.5Missense obs/exp: 185 / 257.8Syn Z: -0.41

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ATCAY · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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