ATAD2

Chr 8

ATPase family AAA domain containing 2

Also known as: ANCCA, CT137, PRO2000

ATAD2 encodes a chromatin-associated ATPase with two AAA domains and a bromodomain that functions as a transcriptional coactivator, particularly for estrogen receptor signaling and cell cycle progression. The gene is highly constrained against loss-of-function variants (pLI 0.998, LOEUF 0.273), but definitive disease associations in humans have not been established. Variants in this gene may potentially affect transcriptional regulation and chromatin remodeling processes.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
24
Pubs (1 yr)
49
P/LP submissions
0%
P/LP missense
0.27
LOEUF· LoF intol.
LOF
Mechanism· predicted
Clinical SummaryATAD2
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
49 unique Pathogenic / Likely Pathogenic· 140 VUS of 231 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.27LOEUF
pLI 0.998
Z-score 6.68
OE 0.17 (0.110.27)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.66Z-score
OE missense 0.83 (0.770.88)
589 obs / 713.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.17 (0.110.27)
00.351.4
Missense OE0.83 (0.770.88)
00.61.4
Synonymous OE1.04
01.21.6
LoF obs/exp: 13 / 75.8Missense obs/exp: 589 / 713.7Syn Z: -0.51
DN
0.3395th %ile
GOF
0.2298th %ile
LOF
0.72top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.27

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

231 submitted variants in ClinVar

Classification Summary

Pathogenic49
VUS140
Likely Benign8
Benign1
49
Pathogenic
140
VUS
8
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
49
0
49
Likely Pathogenic
0
0
0
0
0
VUS
0
139
1
0
140
Likely Benign
0
7
1
0
8
Benign
0
0
1
0
1
Total0146520198

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ATAD2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →