ASNSD1

Chr 2

asparagine synthetase domain containing 1

Also known as: NBLA00058, NS3TP1

This protein is predicted to function as an asparagine synthase, catalyzing asparagine biosynthesis from glutamine. The gene is extremely intolerant to loss-of-function variants (pLI ~1.0), suggesting that mutations likely cause severe developmental disorders, though specific disease associations have not yet been established. Predicted involvement in adipose and skeletal muscle development suggests potential impacts on growth and metabolic function.

OMIMResearchSummary from RefSeq
LOEUF 1.47
Clinical SummaryASNSD1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.47LOEUF
pLI 0.000
Z-score -0.20
OE 1.05 (0.761.47)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.53Z-score
OE missense 0.92 (0.841.01)
312 obs / 339.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.05 (0.761.47)
00.351.4
Missense OE0.92 (0.841.01)
00.61.4
Synonymous OE0.99
01.21.6
LoF obs/exp: 24 / 22.9Missense obs/exp: 312 / 339.5Syn Z: 0.05

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ASNSD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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