ASCC3

Chr 6

activating signal cointegrator 1 complex subunit 3

Also known as: ASC1p200, HELIC1, MRT81, RNAH

This gene encodes a protein that belongs to a family of helicases that are involved in the ATP-dependent unwinding of nucleic acid duplexes. The encoded protein is the largest subunit of the activating signal cointegrator 1 complex that is involved in DNA repair and resistance to alkylation damage. Alternate splicing results in multiple transcript variants. [provided by RefSeq, Sep 2013]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtIntellectual developmental disorder, autosomal recessive 81
0
Active trials
11
Pubs (1 yr)
P/LP submissions
P/LP missense
0.57
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.57LOEUF
pLI 0.000
Z-score 5.58
OE 0.45 (0.360.57)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
2.23Z-score
OE missense 0.82 (0.770.86)
938 obs / 1150.8 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios?
LoF OE?0.45 (0.360.57)
00.351.4
Missense OE?0.82 (0.770.86)
00.61.4
Synonymous OE?1.02
01.21.6
LoF obs/exp: 55 / 121.3Missense obs/exp: 938 / 1150.8Syn Z: -0.37

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ASCC3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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