ASB6

Chr 9

ankyrin repeat and SOCS box containing 6

ASB6 encodes a substrate-recognition component of an E3 ubiquitin ligase complex that targets proteins for degradation, including SQSTM1 which regulates cell proliferation and autophagy. The gene shows low constraint to loss-of-function variants, and no definitive human disease associations have been established in the provided data. Clinical significance of ASB6 variants in pediatric neurological disorders remains unclear.

OMIMResearchSummary from RefSeq, UniProt
GOFmechanismLOEUF 0.97
Clinical SummaryASB6
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.97LOEUF
pLI 0.001
Z-score 1.65
OE 0.52 (0.290.97)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.05Z-score
OE missense 0.82 (0.730.92)
222 obs / 270.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.52 (0.290.97)
00.351.4
Missense OE0.82 (0.730.92)
00.61.4
Synonymous OE1.10
01.21.6
LoF obs/exp: 7 / 13.5Missense obs/exp: 222 / 270.7Syn Z: -0.85
DN
0.5477th %ile
GOF
0.6834th %ile
LOF
0.2680th %ile

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ASB6 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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