ASB17

Chr 1

ankyrin repeat and SOCS box containing 17

Also known as: Asb-17

ASB17 encodes a substrate-recognition component of an E3 ubiquitin-protein ligase complex that mediates proteasomal degradation of target proteins. The gene is highly constrained against loss-of-function variants (pLI = 1.0), but no established human disease associations have been reported for ASB17 mutations.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
1
Pubs (1 yr)
21
P/LP submissions
0%
P/LP missense
1.51
LOEUF
Mechanism
Clinical SummaryASB17
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
21 unique Pathogenic / Likely Pathogenic· 38 VUS of 62 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.51LOEUF
pLI 0.000
Z-score 0.38
OE 0.87 (0.531.51)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.12Z-score
OE missense 1.03 (0.901.17)
154 obs / 150.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.87 (0.531.51)
00.351.4
Missense OE1.03 (0.901.17)
00.61.4
Synonymous OE0.98
01.21.6
LoF obs/exp: 9 / 10.3Missense obs/exp: 154 / 150.0Syn Z: 0.13

ClinVar Variant Classifications

62 submitted variants in ClinVar

Classification Summary

Pathogenic18
Likely Pathogenic3
VUS38
Likely Benign1
18
Pathogenic
3
Likely Pathogenic
38
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
18
0
18
Likely Pathogenic
0
0
3
0
3
VUS
0
33
5
0
38
Likely Benign
0
0
1
0
1
Benign
0
0
0
0
0
Total03327060

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ASB17 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC