ARMC9

Chr 2AR

armadillo repeat containing 9

Also known as: ARM, JBTS30, KU-MEL-1, NS21

Predicted to be involved in cilium assembly and positive regulation of smoothened signaling pathway. Located in centriole and ciliary basal body. Implicated in Joubert syndrome 30. [provided by Alliance of Genome Resources, Jul 2025]

Primary Disease Associations & Inheritance

Joubert syndrome 30MIM #617622
AR
795
ClinVar variants
58
Pathogenic / LP
pLI score
0
Active trials
Clinical SummaryARMC9
📋
ClinVar Variants
58 Pathogenic / Likely Pathogenic· 140 VUS of 795 total submissions
Some data sources returned errors (1)

gnomad: Error: gnomAD API error: 502

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

795 submitted variants in ClinVar

Classification Summary

Pathogenic38
Likely Pathogenic20
VUS140
Likely Benign144
Benign17
Conflicting9
38
Pathogenic
20
Likely Pathogenic
140
VUS
144
Likely Benign
17
Benign
9
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
9
0
29
0
38
Likely Pathogenic
13
4
2
1
20
VUS
3
127
10
0
140
Likely Benign
0
6
72
66
144
Benign
0
8
7
2
17
Conflicting
9
Total2514512069368

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ARMC9 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Gene2Phenotype Curations

ARMC9-related Joubert syndrome

definitive
ARLoss Of FunctionAbsent Gene Product
Dev. DisordersEye
G2P ↗

Gene2Phenotype curations · DECIPHER consortium patient cohort (public variants) · deciphergenomics.org

OMIM — Genotype-Phenotype Relationships

1 OMIM entry

Joubert syndrome 30

MIM #617622

Molecular basis of disorder known

Autosomal recessive
Clinical Literature
Landmark / reviewRecent case evidence
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →