ARK2N

Chr 18

arkadia (RNF111) N-terminal like PKA signaling regulator 2N

Also known as: ARKL1, C18orf25, RNF111L1

This protein functions as an AMPK substrate important for exercise capacity and skeletal muscle function, and is required for normal contraction-induced signaling. The gene is highly constrained against loss-of-function variants (pLI 0.89, LOEUF 0.39), suggesting mutations would likely cause severe disease. However, no specific disease phenotypes associated with ARK2N mutations are currently established in clinical databases.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
3
Pubs (1 yr)
49
P/LP submissions
P/LP missense
0.39
LOEUF
Mechanism
Clinical SummaryARK2N
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.89) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
47 unique Pathogenic / Likely Pathogenic· 3 VUS of 60 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.39LOEUF
pLI 0.890
Z-score 3.24
OE 0.13 (0.050.39)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.55Z-score
OE missense 0.90 (0.801.01)
200 obs / 223.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.13 (0.050.39)
00.351.4
Missense OE0.90 (0.801.01)
00.61.4
Synonymous OE0.84
01.21.6
LoF obs/exp: 2 / 16.0Missense obs/exp: 200 / 223.1Syn Z: 1.18

ClinVar Variant Classifications

60 submitted variants in ClinVar

Classification Summary

Pathogenic45
Likely Pathogenic2
VUS3
Likely Benign1
45
Pathogenic
2
Likely Pathogenic
3
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
45
Likely Pathogenic
2
VUS
3
Likely Benign
1
Benign
0
Total51

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ARK2N · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC