ARID5A

Chr 2

AT-rich interaction domain 5A

Also known as: MRF-1, MRF1, RP11-363D14

This gene encodes a DNA-binding protein that regulates transcription by binding to AT-rich promoter sequences and functions as an RNA-binding protein that stabilizes inflammation-related mRNAs including IL6 and STAT3. Mutations in ARID5A have not been definitively associated with human disease based on the available information. The gene shows high constraint against loss-of-function variants (pLI = 0.95, LOEUF = 0.35), suggesting that complete loss of function would likely be severe if disease-causing.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
11
Pubs (1 yr)
32
P/LP submissions
0%
P/LP missense
0.35
LOEUF
LOF
Mechanism· predicted
Clinical SummaryARID5A
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.95). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
32 unique Pathogenic / Likely Pathogenic· 124 VUS of 169 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.35LOEUF
pLI 0.945
Z-score 3.49
OE 0.11 (0.040.35)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.67Z-score
OE missense 0.75 (0.670.83)
253 obs / 339.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.11 (0.040.35)
00.351.4
Missense OE0.75 (0.670.83)
00.61.4
Synonymous OE0.88
01.21.6
LoF obs/exp: 2 / 18.0Missense obs/exp: 253 / 339.5Syn Z: 1.17
DN
0.3991th %ile
GOF
0.3590th %ile
LOF
0.75top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.35

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

169 submitted variants in ClinVar

Classification Summary

Pathogenic22
Likely Pathogenic10
VUS124
Likely Benign8
Conflicting1
22
Pathogenic
10
Likely Pathogenic
124
VUS
8
Likely Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
22
0
22
Likely Pathogenic
0
0
10
0
10
VUS
2
91
31
0
124
Likely Benign
0
3
3
2
8
Benign
0
0
0
0
0
Conflicting
1
Total294662165

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ARID5A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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