AQP2

Chr 12

aquaporin 2

Also known as: AQP-2, AQP-CD, NDI2, WCH-CD

This gene encodes a water channel protein located in the kidney collecting tubule. It belongs to the MIP/aquaporin family, some members of which are clustered together on chromosome 12q13. Mutations in this gene have been linked to autosomal dominant and recessive forms of nephrogenic diabetes insipidus. [provided by RefSeq, Oct 2008]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtDiabetes insipidus, nephrogenic, 2, autosomal
0
Active trials
104
Pubs (1 yr)
P/LP submissions
P/LP missense
1.57
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — AQP2
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.57LOEUF
pLI 0.000
Z-score 0.26
OE 0.91 (0.551.57)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
1.06Z-score
OE missense 0.78 (0.670.89)
137 obs / 176.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.91 (0.551.57)
00.351.4
Missense OE?0.78 (0.670.89)
00.61.4
Synonymous OE?1.06
01.21.6
LoF obs/exp: 9 / 9.9Missense obs/exp: 137 / 176.6Syn Z: -0.42

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

AQP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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