APBB1IP

Chr 10

amyloid beta precursor protein binding family B member 1 interacting protein

Also known as: INAG1, PREL1, RARP1, RIAM

The APBB1IP protein mediates signal transduction from Ras activation to actin cytoskeletal remodeling and plays a role in Rap1-induced cell adhesion. This gene is highly constrained against loss-of-function mutations (pLI 0.85, LOEUF 0.37), suggesting that pathogenic variants would likely cause significant developmental or neurological phenotypes. However, no established human disease phenotype has been definitively linked to APBB1IP mutations in current medical literature.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
3
Pubs (1 yr)
10
P/LP submissions
0%
P/LP missense
0.37
LOEUF
Mechanism
Clinical SummaryAPBB1IP
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.85) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
10 unique Pathogenic / Likely Pathogenic· 87 VUS of 123 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.37LOEUF
pLI 0.854
Z-score 4.06
OE 0.18 (0.090.37)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.29Z-score
OE missense 0.80 (0.720.88)
253 obs / 317.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.18 (0.090.37)
00.351.4
Missense OE0.80 (0.720.88)
00.61.4
Synonymous OE1.19
01.21.6
LoF obs/exp: 5 / 28.3Missense obs/exp: 253 / 317.4Syn Z: -1.68

ClinVar Variant Classifications

123 submitted variants in ClinVar

Classification Summary

Pathogenic9
Likely Pathogenic1
VUS87
Likely Benign6
Benign5
9
Pathogenic
1
Likely Pathogenic
87
VUS
6
Likely Benign
5
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
9
0
9
Likely Pathogenic
0
0
1
0
1
VUS
0
85
2
0
87
Likely Benign
0
4
0
2
6
Benign
0
3
1
1
5
Total092133108

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

APBB1IP · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC