APBA1

Chr 9

amyloid beta precursor protein binding family A member 1

Also known as: D9S411E, LIN10, MINT1, X11, X11A, X11ALPHA

The protein functions as a neuronal adapter protein that regulates synaptic vesicle exocytosis and transports NMDA receptor subunits along microtubules, while also modulating amyloid precursor protein processing. Mutations cause autosomal dominant intellectual disability with variable neurological features. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.388), suggesting that complete loss of protein function is poorly tolerated.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.39
Clinical SummaryAPBA1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.54) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.39LOEUF
pLI 0.537
Z-score 4.44
OE 0.21 (0.130.39)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.23Z-score
OE missense 0.73 (0.680.80)
404 obs / 551.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.21 (0.130.39)
00.351.4
Missense OE0.73 (0.680.80)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 8 / 37.2Missense obs/exp: 404 / 551.4Syn Z: -0.40

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

APBA1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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