AP4M1

Chr 7AR

adaptor related protein complex 4 subunit mu 1

Also known as: CPSQ3, MU-4, MU-ARP2, SPG50

This gene encodes a subunit of the heterotetrameric AP-4 complex. The encoded protein belongs to the adaptor complexes medium subunits family. This AP-4 complex is involved in the recognition and sorting of cargo proteins with tyrosine-based motifs from the trans-golgi network to the endosomal-lysosomal system. [provided by RefSeq, Jul 2008]

OMIMResearchGenerating clinical summary…
LOFmechanismARLOEUF 1.311 OMIM phenotype
Clinical SummaryAP4M1
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Gene-Disease Validity (ClinGen)
AP-4 deficiency syndrome · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
4 active or recruiting trials — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.31LOEUF
pLI 0.000
Z-score 0.26
OE 0.95 (0.691.31)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-1.21Z-score
OE missense 1.21 (1.101.33)
311 obs / 256.4 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.95 (0.691.31)
00.351.4
Missense OE?1.21 (1.101.33)
00.61.4
Synonymous OE?1.39
01.21.6
LoF obs/exp: 26 / 27.5Missense obs/exp: 311 / 256.4Syn Z: -3.23

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

AP4M1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.