AOPEP

Chr 9AR

aminopeptidase O (putative)

Also known as: AP-O, APO, C90RF3, C9orf3, DYT31, ONPEP

The protein is an aminopeptidase that cleaves amino acid residues from the N-terminus of peptides and proteins. Mutations cause dystonia 31, an autosomal recessive movement disorder. The gene shows minimal constraint against loss-of-function variants, which is consistent with the recessive inheritance pattern.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.941 OMIM phenotype
Clinical SummaryAOPEP
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.94LOEUF
pLI 0.000
Z-score 1.87
OE 0.69 (0.510.94)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.46Z-score
OE missense 0.94 (0.861.02)
411 obs / 438.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.69 (0.510.94)
00.351.4
Missense OE0.94 (0.861.02)
00.61.4
Synonymous OE0.95
01.21.6
LoF obs/exp: 29 / 42.1Missense obs/exp: 411 / 438.2Syn Z: 0.49

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

AOPEP · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC