ANO3

Chr 11

anoctamin 3

Also known as: C11orf25, DYT23, DYT24, GENX-3947, TMEM16C

The protein encoded by this gene belongs to the TMEM16 family of predicted membrane proteins, that are also known as anoctamins. While little is known about the function of this gene, mutations in this gene have been associated with some cases of autosomal dominant craniocervical dystonia. Cells from individuals with a mutation in this gene exhibited abnormalities in endoplasmic reticulum-dependent calcium signaling. Studies in rat show that the rat ortholog of this protein interacts with, and modulates the activity of a sodium-activated potassium channel. Deletion of this gene caused increased pain sensitivity in the rat model system. Alternative splicing results in multiple transcript variants encoding different isoforms. [provided by RefSeq, Aug 2015]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtDystonia 24
0
Active trials
14
Pubs (1 yr)
P/LP submissions
P/LP missense
0.77
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — ANO3
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.77LOEUF
pLI 0.000
Z-score 3.11
OE 0.58 (0.450.77)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
2.46Z-score
OE missense 0.70 (0.650.76)
378 obs / 538.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios?
LoF OE?0.58 (0.450.77)
00.351.4
Missense OE?0.70 (0.650.76)
00.61.4
Synonymous OE?1.01
01.21.6
LoF obs/exp: 38 / 65.0Missense obs/exp: 378 / 538.4Syn Z: -0.15

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ANO3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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