ANKRD42

Chr 11

ankyrin repeat domain 42

Also known as: PPP1R79, SARP

The protein is predicted to bind NF-kappaB and inhibit cyclin-dependent protein kinases, acting to positively regulate NF-kappaB transcription and inflammatory cytokine production in the nucleus. This gene is extremely intolerant to loss-of-function variation (pLI near 1.0), indicating mutations likely cause severe developmental disorders, though specific associated phenotypes have not yet been established in clinical databases. The high constraint suggests mutations would be expected to cause early-onset neurodevelopmental abnormalities.

OMIMResearchSummary from RefSeq
GOFmechanismLOEUF 1.23
Clinical SummaryANKRD42
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.23LOEUF
pLI 0.000
Z-score 0.76
OE 0.82 (0.561.23)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.13Z-score
OE missense 0.97 (0.871.09)
205 obs / 210.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.82 (0.561.23)
00.351.4
Missense OE0.97 (0.871.09)
00.61.4
Synonymous OE0.88
01.21.6
LoF obs/exp: 17 / 20.7Missense obs/exp: 205 / 210.5Syn Z: 0.78
DN
0.5966th %ile
GOF
0.6833th %ile
LOF
0.3939th %ile

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ANKRD42 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found