ANKRD28

Chr 3

ankyrin repeat domain 28

Also known as: CFAP79, FAP79, PITK, PPP1R65

ANKRD28 encodes a regulatory subunit of protein phosphatase 6 (PP6) that controls dephosphorylation of various substrates including NFKBIE, MOB1, and HNRPK, and also selectively inhibits protein phosphatase 1C (PPP1C). The gene is highly constrained against loss-of-function variants (pLI 1.0, LOEUF 0.17), suggesting mutations would likely cause severe developmental disorders. However, no specific disease associations or inheritance patterns have been established for this gene.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.17
Clinical SummaryANKRD28
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
23 unique Pathogenic / Likely Pathogenic· 143 VUS of 221 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.17LOEUF
pLI 1.000
Z-score 6.27
OE 0.07 (0.040.17)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.39Z-score
OE missense 0.71 (0.660.78)
390 obs / 547.1 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.07 (0.040.17)
00.351.4
Missense OE0.71 (0.660.78)
00.61.4
Synonymous OE0.88
01.21.6
LoF obs/exp: 4 / 53.5Missense obs/exp: 390 / 547.1Syn Z: 1.28

ClinVar Variant Classifications

221 submitted variants in ClinVar

Classification Summary

Pathogenic22
Likely Pathogenic1
VUS143
Likely Benign17
Benign1
22
Pathogenic
1
Likely Pathogenic
143
VUS
17
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
22
0
22
Likely Pathogenic
0
0
1
0
1
VUS
0
141
2
0
143
Likely Benign
0
3
4
10
17
Benign
1
0
0
0
1
Total11442910184

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ANKRD28 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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