ANKRD10

Chr 13

ankyrin repeat domain 10

ANKRD10 encodes a nucleoplasm-localized protein predicted to be involved in protein targeting to chloroplast. Mutations cause autosomal recessive intellectual disability with seizures and cortical blindness. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.62), and affected individuals typically present in infancy with developmental delays and neurological complications.

ResearchSummary from RefSeq
DNmechanismLOEUF 0.62
Clinical SummaryANKRD10
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.27) despite low pLI — interpret in context.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.62LOEUF
pLI 0.165
Z-score 2.61
OE 0.27 (0.130.62)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.35Z-score
OE missense 0.76 (0.670.85)
183 obs / 242.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.27 (0.130.62)
00.351.4
Missense OE0.76 (0.670.85)
00.61.4
Synonymous OE1.06
01.21.6
LoF obs/exp: 4 / 14.9Missense obs/exp: 183 / 242.1Syn Z: -0.50
DN
0.6453th %ile
GOF
0.6150th %ile
LOF
0.4726th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ANKRD10 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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