AMHR2

Chr 12AR

anti-Mullerian hormone receptor type 2

Also known as: AMHR, MISR2, MISRII, MRII

This gene encodes the receptor for the anti-Mullerian hormone (AMH) which, in addition to testosterone, results in male sex differentiation. AMH and testosterone are produced in the testes by different cells and have different effects. Testosterone promotes the development of male genitalia while the binding of AMH to the encoded receptor prevents the development of the mullerian ducts into uterus and Fallopian tubes. Mutations in this gene are associated with persistent Mullerian duct syndrome type II. Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq, Sep 2009]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Persistent Mullerian duct syndrome, type IIMIM #261550
AR
UniProtPersistent Muellerian duct syndrome 2
0
Active trials
60
Pubs (1 yr)
P/LP submissions
P/LP missense
0.93
LOEUF
Multiple*
Mechanism· predicted
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.93LOEUF
pLI 0.000
Z-score 1.85
OE 0.64 (0.450.93)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.39Z-score
OE missense 0.94 (0.851.03)
293 obs / 312.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.64 (0.450.93)
00.351.4
Missense OE?0.94 (0.851.03)
00.61.4
Synonymous OE?0.88
01.21.6
LoF obs/exp: 20 / 31.1Missense obs/exp: 293 / 312.6Syn Z: 1.05

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

AMHR2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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