ALPK1

Chr 4AD

alpha kinase 1

Also known as: 8430410J10Rik, LAK, ROSAH

This gene encodes an alpha kinase. Mice which were homozygous for disrupted copies of this gene exhibited coordination defects (PMID: 21208416). Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Dec 2011]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

ROSAH syndromeMIM #614979
AD
UniProtRetinal dystrophy, optic nerve edema, splenomegaly, anhidrosis, and migraine headache syndrome

Clinical highlights

Gene-disease validity (ClinGen)
retinal dystrophy, optic nerve edema, splenomegaly, anhidrosis, and migraine headache syndrome · ADDefinitivesufficient evidence for diagnostic panels
3
Active trials
46
Pubs (1 yr)
P/LP submissions
P/LP missense
0.93
LOEUF
Multiple*
Mechanism· predicted
📖
GeneReview available — ALPK1
Authoritative clinical overview · Recommended first read
Open GeneReview ↗

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.93LOEUF
pLI 0.000
Z-score 1.98
OE 0.71 (0.550.93)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
-0.28Z-score
OE missense 1.03 (0.971.10)
680 obs / 659.6 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.71 (0.550.93)
00.351.4
Missense OE?1.03 (0.971.10)
00.61.4
Synonymous OE?0.96
01.21.6
LoF obs/exp: 38 / 53.6Missense obs/exp: 680 / 659.6Syn Z: 0.47

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ALPK1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.