ALOXE3

Chr 17AR

arachidonate epidermal lipoxygenase 3

The protein is a hydroperoxide isomerase that synthesizes epoxy-alcohol derivatives from fatty acid precursors and plays a crucial role in establishing the skin barrier by modifying ceramides in the lipid envelope of skin cells. Mutations cause congenital ichthyosis with autosomal recessive inheritance, presenting as scaling and erythroderma from birth due to impaired skin barrier function. The gene shows low constraint against loss-of-function variants (LOEUF 1.055), consistent with the recessive inheritance pattern where heterozygous carriers are typically unaffected.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 1.051 OMIM phenotype
Clinical SummaryALOXE3
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.05LOEUF
pLI 0.000
Z-score 1.26
OE 0.80 (0.611.05)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.15Z-score
OE missense 0.98 (0.911.06)
471 obs / 480.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.80 (0.611.05)
00.351.4
Missense OE0.98 (0.911.06)
00.61.4
Synonymous OE0.96
01.21.6
LoF obs/exp: 35 / 44.0Missense obs/exp: 471 / 480.2Syn Z: 0.41

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ALOXE3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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