ALDOC

Chr 17

aldolase, fructose-bisphosphate C

Also known as: ALDC

The protein catalyzes the reversible conversion of fructose-1,6-bisphosphate into two triose phosphates and plays a key role in glycolysis and gluconeogenesis, with specific expression in hippocampus and Purkinje cells. Mutations cause disease through a dominant-negative mechanism. The inheritance pattern and specific disease phenotype are not established in the provided data.

Summary from RefSeq, UniProt, Mechanism
0
Active trials
24
Pubs (1 yr)
6
P/LP submissions
0%
P/LP missense
LOEUF
DN
Mechanism· predicted
Clinical SummaryALDOC
📋
ClinVar Variants
6 unique Pathogenic / Likely Pathogenic· 47 VUS of 62 total submissions
Some data sources returned errors (1)

gnomad: Error: gnomAD API error: 502

Population Genetics & Constraint

Constraint data not available from gnomAD.

DN
0.74top 25%
GOF
0.6051th %ile
LOF
0.2580th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

62 submitted variants in ClinVar

Classification Summary

Pathogenic5
Likely Pathogenic1
VUS47
Likely Benign3
Benign1
5
Pathogenic
1
Likely Pathogenic
47
VUS
3
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
5
0
5
Likely Pathogenic
0
0
1
0
1
VUS
0
43
4
0
47
Likely Benign
0
1
0
2
3
Benign
0
0
1
0
1
Total04411257

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ALDOC · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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