ALDOA

Chr 16

aldolase, fructose-bisphosphate A

Also known as: ALDA, GSD12, HEL-S-87p

This gene encodes a member of the class I fructose-bisphosphate aldolase protein family. The encoded protein is a glycolytic enzyme that catalyzes the reversible conversion of fructose-1,6-bisphosphate to glyceraldehyde 3-phosphate and dihydroxyacetone phosphate. Three aldolase isozymes (A, B, and C), encoded by three different genes, are differentially expressed during development. Mutations in this gene have been associated with Glycogen Storage Disease XII, an autosomal recessive disorder associated with hemolytic anemia. Disruption of this gene also plays a role in the progression of multiple types of cancers. Related pseudogenes have been identified on chromosomes 3 and 10. [provided by RefSeq, Sep 2017]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtGlycogen storage disease 12
0
Active trials
110
Pubs (1 yr)
P/LP submissions
P/LP missense
0.76
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.76LOEUF
pLI 0.001
Z-score 2.36
OE 0.42 (0.240.76)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.26Z-score
OE missense 0.95 (0.861.06)
235 obs / 246.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.42 (0.240.76)
00.351.4
Missense OE?0.95 (0.861.06)
00.61.4
Synonymous OE?1.32
01.21.6
LoF obs/exp: 8 / 19.1Missense obs/exp: 235 / 246.4Syn Z: -2.52

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ALDOA · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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