AKR1E2

Chr 10

aldo-keto reductase family 1 member E2

Also known as: AKR1CL2, AKRDC1, HTSP1, LoopADR, TAKR, hTSP, htAKR

The protein is an aldo-keto reductase that catalyzes the NADPH-dependent reduction of 1,5-anhydro-D-fructose to 1,5-anhydro-D-glucitol and has low reductase activity towards other substrates. This gene is not highly constrained against loss-of-function variants and is not currently associated with any established Mendelian disease phenotypes in major clinical databases.

OMIMResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 1.42
Clinical SummaryAKR1E2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.42LOEUF
pLI 0.000
Z-score 0.21
OE 0.95 (0.651.42)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.31Z-score
OE missense 1.07 (0.951.20)
188 obs / 176.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.95 (0.651.42)
00.351.4
Missense OE1.07 (0.951.20)
00.61.4
Synonymous OE0.74
01.21.6
LoF obs/exp: 17 / 18.0Missense obs/exp: 188 / 176.3Syn Z: 1.68
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedAKR1E2-related congenital cataractOTHERAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.76top 25%
GOF
0.6540th %ile
LOF
0.2581th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

AKR1E2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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