AKR1E2

Chr 10

aldo-keto reductase family 1 member E2

Also known as: AKR1CL2, AKRDC1, HTSP1, LoopADR, TAKR, hTSP, htAKR

The protein encoded by this gene is a member of the aldo-keto reductase superfamily. Members in this family are characterized by their structure (evolutionarily highly conserved TIM barrel) and function (NAD(P)H-dependent oxido-reduction of carbonyl groups). Transcripts of this gene have been reported in specimens of human testis. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2012]

0
Active trials
3
Pubs (1 yr)
15
P/LP submissions
0%
P/LP missense
1.42
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryAKR1E2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
15 unique Pathogenic / Likely Pathogenic· 74 VUS of 200 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.42LOEUF
pLI 0.000
Z-score 0.21
OE 0.95 (0.651.42)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.31Z-score
OE missense 1.07 (0.951.20)
188 obs / 176.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.95 (0.651.42)
00.351.4
Missense OE1.07 (0.951.20)
00.61.4
Synonymous OE0.74
01.21.6
LoF obs/exp: 17 / 18.0Missense obs/exp: 188 / 176.3Syn Z: 1.68
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedAKR1E2-related congenital cataractOTHERAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.76top 25%
GOF
0.6540th %ile
LOF
0.2581th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

200 submitted variants in ClinVar

Classification Summary

Pathogenic14
Likely Pathogenic1
VUS74
Likely Benign15
Benign79
14
Pathogenic
1
Likely Pathogenic
74
VUS
15
Likely Benign
79
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
14
0
14
Likely Pathogenic
0
0
1
0
1
VUS
1
65
8
0
74
Likely Benign
2
2
11
0
15
Benign
0
3
72
4
79
Total3701064183

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

AKR1E2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found