AKR1C8

Chr 10

aldo-keto reductase family 1 member C8

Also known as: AKR1C8P, AKR1CL1

The protein is an aldo-keto reductase that catalyzes NADPH-dependent reduction reactions and estradiol 17-beta-dehydrogenase activity, participating in prostaglandin biosynthesis. No disease-causing mutations in this gene have been reported in humans to date.

ResearchSummary from RefSeq
Multiplemechanism
Clinical SummaryAKR1C8
📋
ClinVar Variants
14 unique Pathogenic / Likely Pathogenic· 3 VUS of 24 total submissions
Some data sources returned errors (1)

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

DN
0.7230th %ile
GOF
0.6639th %ile
LOF
0.2871th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

24 submitted variants in ClinVar

Classification Summary

Pathogenic12
Likely Pathogenic2
VUS3
Likely Benign4
Benign1
12
Pathogenic
2
Likely Pathogenic
3
VUS
4
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
12
Likely Pathogenic
2
VUS
3
Likely Benign
4
Benign
1
Total22

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

AKR1C8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found