AKR1C4

Chr 10

aldo-keto reductase family 1 member C4

Also known as: 3-alpha-HSD, C11, CDR, CHDR, DD-4, DD4, HAKRA

This gene encodes a member of the aldo/keto reductase superfamily, which consists of more than 40 known enzymes and proteins. These enzymes catalyze the conversion of aldehydes and ketones to their corresponding alcohols by utilizing NADH and/or NADPH as cofactors. The enzymes display overlapping but distinct substrate specificity. This enzyme catalyzes the bioreduction of chlordecone, a toxic organochlorine pesticide, to chlordecone alcohol in liver. This gene shares high sequence identity with three other gene members and is clustered with those three genes at chromosome 10p15-p14. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProt46,XY sex reversal 8
0
Active trials
20
Pubs (1 yr)
P/LP submissions
P/LP missense
1.72
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.72LOEUF
pLI 0.000
Z-score -0.92
OE 1.23 (0.881.72)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-1.04Z-score
OE missense 1.22 (1.091.37)
214 obs / 175.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.23 (0.881.72)
00.351.4
Missense OE?1.22 (1.091.37)
00.61.4
Synonymous OE?1.15
01.21.6
LoF obs/exp: 23 / 18.7Missense obs/exp: 214 / 175.2Syn Z: -0.95

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

AKR1C4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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