AKR1C1

Chr 10

aldo-keto reductase family 1 member C1

Also known as: 2-ALPHA-HSD, 20-ALPHA-HSD, DD1, DD1/DD2, DDH, DDH1, H-37, HAKRC

This gene encodes a member of the aldo/keto reductase superfamily, which consists of more than 40 known enzymes and proteins. These enzymes catalyze the conversion of aldehydes and ketones to their corresponding alcohols by utilizing NADH and/or NADPH as cofactors. The enzymes display overlapping but distinct substrate specificity. This enzyme catalyzes the reaction of progesterone to the inactive form 20-alpha-hydroxy-progesterone. This gene shares high sequence identity with three other gene members and is clustered with those three genes at chromosome 10p15-p14. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…
0
Active trials
72
Pubs (1 yr)
P/LP submissions
P/LP missense
1.59
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.59LOEUF
pLI 0.000
Z-score -0.43
OE 1.11 (0.781.59)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-1.42Z-score
OE missense 1.31 (1.171.47)
211 obs / 160.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.11 (0.781.59)
00.351.4
Missense OE?1.31 (1.171.47)
00.61.4
Synonymous OE?1.31
01.21.6
LoF obs/exp: 21 / 19.0Missense obs/exp: 211 / 160.5Syn Z: -1.85

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

AKR1C1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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