AKIRIN1

Chr 1

akirin 1

Also known as: C1orf108, STRF2

AKIRIN1 encodes a nuclear transcriptional coregulator that functions as a molecular adapter in skeletal muscle development and regeneration, serving as a signal transducer for myostatin and regulating myoblast and macrophage chemotaxis through actin cytoskeleton reorganization. The gene is highly constrained against loss-of-function variants, but no definitive human disease associations have been established in the current literature. Any potential disorders would likely involve skeletal muscle development or regeneration given the protein's specific functional role.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.50
Clinical SummaryAKIRIN1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.79) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.50LOEUF
pLI 0.793
Z-score 2.57
OE 0.10 (0.040.50)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.50Z-score
OE missense 0.85 (0.701.03)
71 obs / 83.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.10 (0.040.50)
00.351.4
Missense OE0.85 (0.701.03)
00.61.4
Synonymous OE1.11
01.21.6
LoF obs/exp: 1 / 9.6Missense obs/exp: 71 / 83.9Syn Z: -0.45
DN
0.5279th %ile
GOF
0.3788th %ile
LOF
0.69top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.50

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

AKIRIN1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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